Startle disease—hyperekplexia (two sibling cases)

نویسندگان

  • Şakìr Altunbaşak
  • Vildan Baytok
چکیده

Two sisters aged 12 and 13 applied to our hospital with complaints of jerking tonic contraction triggered by sudden noise. Diffuse bilaterally polyspike-wave discharges appeared on waking electroencephalography and during that time a startle-induced tonic contraction was seen. Their neurological examinations and neuro-radiological imaging were normal except for hyperreflexia. We presented these cases because of being rare.

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عنوان ژورنال:
  • Seizure

دوره 5  شماره 

صفحات  -

تاریخ انتشار 1996